Hip abduction and supported standing affect the ranges of hips extension in spinal muscular atrophy patients
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Department of Rehabilitation, Józef Piłsudski University of Physical Education, Warsaw, Poland
Center of Functional Rehabilitation Orthos, Warsaw, Poland
Institute of Physiotherapy, Faculty of Health Sciences, The Jan Kochanowski University, Kielce, Poland
Katarzyna Maślanko   

Center of Functional Rehabilitation Orthos, Warsaw, Poland
Submission date: 2020-07-28
Final revision date: 2020-10-12
Acceptance date: 2020-10-12
Online publication date: 2020-12-09
Pol. Ann. Med. 2021;28(1):50–56
Recommendations for management of spinal muscular atrophy (SMA) do not contain detailed information about the position of lower limbs during support standing. It has been observed that during the measurement of the range of extension in the hip joint (HE) in SMA patients, the examined limb was often naturally abducted.

The main aim of the study was to compare the values of HE in the sagittal plane and in abduction, and to assess the correlation between the duration of supported standing and HE in SMA patients.

Material and methods:
The study group consisted of 75 SMA individuals aged 2–22 years and control group consisted of 202 healthy participants. The measurements were performed with the Rippstein plurimeter and goniometer.

Results and discussion:
Range of HE in SMA patients was larger in abduction than in the sagittal plane. A correlation was noted between the duration of supported standing and HE.

Supported standing with hip joint abduction should be used in SMA patients. The obtained results broaden the knowledge about the biomechanics of hip joints in SMA patients.

We are thankful to all the participants and their parents for participating in the research. We want to express our thanks to the SMA Foundation Poland for cooperation and help in organizing the project.
The work (costs of translation) was supported by the Ministry of Science and Higher Education in 2017 as a research project of the University of Physical Education in Warsaw (DS-258).
The authors declare that there is no conflict of interest.
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